A case of multiple xanthomatosis

Abstract

Reticulo-xanthomatosis, or Christian-Schueller's disease, which is rare, is characterized by spleno-hepatomegaly, diabetes insipidus, bug-eyed, destruction of flat bones. It occurs more often in children of 4-5 years of age, less often in adults. The symptoms of the disease are directly related to xanthomatous infiltration of the skull bones, mainly the eye socket and the Turkish saddle. The lesion of the skull is a classic sign and is designated by Schueller as a landkart-shaped skull.

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