Lymphangioleiomyomatosis of the lungs: features of the clinical picture, diagnosis and treatment. Case report
- Authors: Ignatova G.L.1, Blinova E.V.1, Bel'sner M.S.1
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Affiliations:
- South Ural State Medical University
- Issue: Vol 24, No 3 (2022)
- Pages: 166-169
- Section: Articles
- URL: https://ogarev-online.ru/2075-1753/article/view/108060
- DOI: https://doi.org/10.26442/20751753.2022.3.201504
- ID: 108060
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Abstract
The article highlights the main issues of etiology, pathogenesis, clinical picture, diagnosis and treatment of patients with lymphangioleiomyomatosis. The clinical observation presents the features of the condition, the rate of progression, diagnostic approaches and management programs for a patient with a rare cystic lung pathology.
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##article.viewOnOriginalSite##About the authors
Galina L. Ignatova
South Ural State Medical University
Email: iglign@mail.ru
ORCID iD: 0000-0002-0877-6554
D. Sci. (Med.), Prof.
Russian Federation, ChelyabinskElena V. Blinova
South Ural State Medical University
Author for correspondence.
Email: blinel@mail.ru
ORCID iD: 0000-0003-2507-5941
Cand. Sci. (Med.)
Russian Federation, ChelyabinskMariia S. Bel'sner
South Ural State Medical University
Email: mariika_04@mail.ru
Cand. Sci. (Med.)
Russian Federation, ChelyabinskReferences
- Meraj R, Wikenheiser-Brokamp KA, Young LR, McCormack FX. Lymphangioleiomyomatosis: new concepts in pathogenesis, diagnosis, and treatment. Semin Respir Crit Care Med. 2012;33(5):486-947. doi: 10.1055/s-0032-1325159
- Ando K, Tobino K, Kurihara M, et al. Quantitative CT analysis of small pulmonary vessels in lymphangioleiomyomatosis. Eur J Radiol. 2012;81(12):3925-30. doi: 10.1016/j.ejrad.2012.05.033
- Seibert D, Hong CH, Takeuchi F, et al. Recognition of tuberous sclerosis in adult women: delauyed presentation with life-treatening consequences. Ann Intern Med. 2011;154(12):806-13,W-294. doi: 10.7326/0003-4819-154-12-201106210-00008
- Zhang X, Travis WD. Pulmonary lymphangioleiomyomatosis. Arch Pathol Lab Med. 2010;134(12):1823-8. doi: 10.5858/2009-0576-RS.1
- Johnson SR, Cordier JF, Lazor R, et al. Review Panel of the ERS LAM Task Force. European Respiratory Society guidelines for the diagnosis and management of lymphangioleiomyomatosis. Eur Respir J. 2010;35(26):14-26. doi: 10.1183/09031936.00076209
- Harari S, Torre O, Moss J. Lymphangioleiomyomatosis: what do we know and what are we looking for? Eur Respir J. 2011;20(119):34-44. doi: 10.1183/09059180.00011010
- Cordier JF, Johnson SR. Multiple cystic lung diseases. Eur Respir Monogr. 2011;54:46-83.
- McCormack FX, Inoue Y, Moss J, et al. Efficacy and safety of sirolimus in lymphangioleiomyomatosis. N Engl J Med. 2011;364:1595-606. doi: 10.1056/NEJMoa1100391
- Kpodonu J, Massad MG, Chaer RA, et al. The US experience with lung transplantation for pulmonary lymphangioleiomyomatosis. J Heart Lung Transplant. 2005; 24(9):1247-53. doi: 10.1016/j.healun.2004.09.013
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